RECIPES ® ® ® KOOL-AID -FLAVORED GLUTAREX -1 FRUIT JUICE-FLAVORED GLUTAREX -2 Yield: 8 fl oz Yield: 8 fl oz 40 g Glutarex-1 20 g Glutarex-2 1 1 3 Tbsp, level, sugar 3 fl oz concentrated apple, grape, or orange juice ® 2 1/4 tsp Kool-Aid or Wyler’s Unsweetened Soft Drink Mix Water (room temperature) to make 8 fl oz Add water (room temperature) to ingredients tomake 8 fl oz. Warm juice concentrate to room temperature. Place all Mix in a blender at lowest speed no more than 4 seconds. Or, ingredients in a 1 blender at lowest speed no more than 4 shake briskly in a closed container for 10 to 12 seconds. Serve seconds. Or, shake briskly in a closed container for 10 to 12 chilled. seconds. Serve chilled. Nutrient 1 fl oz 8 fl oz Nutrient Apple Grape Orange Lysine, mg 0 0 juice juice juice Tryptophan, mg 0 0 Lysine, mg 33 13 33 Protein, g 0.75 6 Tryptophan, mg 6 NA 8 Energy, kcal 42 336 Protein, g 6.5 6.7 8.6 1 Osmolality (concentration of particles in solution) may be too high if more Energy, kcal 257 275 252 sugar is added, which may cause bloating and diarrhea. 2 The amount of drink mix may be varied according to taste preference. ® ® ADDITIONAL TIPS FOR FLAVORING GLUTAREX KOOL-AID -FLAVORED GLUTAREX -2 MEDICAL FOOD Yield: 16 fl oz • Add chocolate or strawberry syrup. 40 g Glutarex-2 1 • Mix Glutarex with fruit to make a “smoothie.” 3 Tbsp, level, sugar 1/2 tsp Kool-Aid or Wyler’s Unsweetened Soft Drink Mix2 • Freeze flavored medical food into “slushies” or “popsicles.” Add water to ingredients to make 16 fl oz. Mix in a blender at • Add dry Glutarex to pudding (lemon, tapioca, vanilla, etc) lowest speed no more than 4 seconds. Or, shake briskly in a mixture. Prepare pudding with non—dairy creamer. closed container for 10 to 12 seconds. Serve chilled. Use low-protein food lists to calculate protein content of Nutrient 16 fl oz flavorings. Lysine,, mg 0 Tryptophan, mg 0 Protein, g 12 Energy, kcal 308 1 Osmolality (concentration of particles in solution) may be too high if more sugar is added, which may cause bloating and diarrhea. 2 The amount of drink mix may be varied according to taste preference. Kool-Aid & Wyler’s are not registered tradmarks of Abbott Laboratories. 70 71
A Food List for Glutaric Aciduria Type 1 (GA 1) Page 35 Page 37