IMPORTANT PHONE NUMBERS CONTENTS Introduction . . . . . . . . . . . . . . . . . . . . . . . . . . 4 Metabolic Dietitian: Food Guide for MMA . . . . . . . . . . . . . . . . . . . . . 4 ILE, MET, THR, VAL, and Odd-Chain Fats in the Body. . .4 Metabolic Physician: Tips . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 7 Other: Food Lists . . . . . . . . . . . . . . . . . . . . . . . . . . . .9 Baby Foods: Serving Lists for ILE-, MET-, THR-, and Goals: VAL-Restricted Foods . . . . . . . . . . . . . . . . . 10 ___________________________________________________________________________________________________ Table Foods: ILE-, MET-, THR-, and VAL-Restricted Foods: . . . . . . . . . . . . . . . . . 26 ___________________________________________________________________________________________________ Breads/Cereals . . . . . . . . . . . . . . . . . . . . . 26 Fats . . . . . . . . . . . . . . . . . . . . . . . . . . . . 36 ___________________________________________________________________________________________________ Fruits . . . . . . . . . . . . . . . . . . . . . . . . . . . 38 ___________________________________________________________________________________________________ Vegetables. . . . . . . . . . . . . . . . . . . . . . . . 46 Free Foods A . . . . . . . . . . . . . . . . . . . . . . 56 ___________________________________________________________________________________________________ Free Foods B. . . . . . . . . . . . . . . . . . . . . . . 60 Low Protein . . . . . . . . . . . . . . . . . . . . . . . 62 ___________________________________________________________________________________________________ Recipes. . . . . . . . . . . . . . . . . . . . . . . . . . 70 ___________________________________________________________________________________________________ Resources . . . . . . . . . . . . . . . . . . . . . . . . 72 TABLES ___________________________________________________________________________________________________ ® Table 1. Preparation of Propimex Medical Food. . . . . .5 ___________________________________________________________________________________________________ Table 2. Measurement Equivalents. . . . . . . . . . . . . .8 Table 3. Metric Conversion Factors . . . . . . . . . . . . . 9 ___________________________________________________________________________________________________ ___________________________________________________________________________________________________ ___________________________________________________________________________________________________ 2 3

A Food List for Methylmalonic Acidemia (MMA) - Page 2 A Food List for Methylmalonic Acidemia (MMA) Page 1 Page 3