RECIPES RESOURCES ® ® ® Kool-Aid -Flavored I-Valex -1 Fruit Juice-Flavored I-Valex -2 Support Groups/Newsletters Ener-G® Foods, Inc. Yield: 8 fl oz Yield: 8 fl oz Organic Acidemia Association 5960 First Avenue South 40 g I-Vales-1 20 g I-Valex-2 9040 Duluth St. Seattle, WA 98108 3 Tbsp, level, sugar1 3 fl oz concentrated apple, grape, or orange juice Golden Valley, MN 55427 Phone: (800) 331-5222; (206) 767-3928 1/4 tsp Kool-Aid or Wyler’s® Unsweetened Soft Drink Mix Water (room temperature) to make 8 fl oz Phone: (763) 559-1797 (Central Time) Fax: (206) 764-3398 Add water (room temperature) to ingredients to make Warm juice concentrate to room temperature. Place all Fax: (866) 539-4060 (Toll Free) Email: [email protected] 8 fl oz. Mix in a blender at lowest speed no more than 4 ingredients in a blender at lowest speed no more than 4 Email: [email protected] Website: ener-g.com seconds. Or, shake briskly in a closed container for 10 to seconds. Or, shake briskly in a closed container for 10 Website: oaanews.org Med-Diet® Laboratories, Inc. 12 seconds. Serve chilled. to 12 seconds. Serve chilled. 3600 Holly Lane, Suite 80 Nutrient 1 fl oz 8 fl oz Nutrient Apple Grape Orange Low-Protein Food Suppliers Plymouth, MN 55447 Lysine, mg 0 0 juice juice juice Canbrands Specialty Foods, Inc. Phone: (800) 633-3438 (MED-DIET); Protein, g 0.75 6 Lysine, mg 33 15 48 3500 Laird Rd. Unit 4 (763) 550-2020 Energy, kcal 42 336 Protein, g 6.5 6.7 8.6 Mississauga, ON, Canada L5L 5Y4 Fax: (763) 550-2022 Energy, kcal 257 275 252 Phone: (905) 829-6003 Email: [email protected] 1 Email: [email protected] Website: med-diet.com Osmolality (concentration of particles in solution) may be too high if more sugar is added, which may cause bloating and diarrhea. Website: canbrands.ca 2 The amount of drink mix may be varied according to taste preference. *Please check with your dietitian or doctor before using this recipe in infants. PKU Perspectives Dietary Specialties Lindon, UT 84042 8 S. Commons Rd. Phone/Text/Fax: (866) 758-3663 Waterbury, CT 06704 Email: [email protected] ® ® Additional Tips for Flavoring I-Valex Phone: (888) 640-2800 Website: pkuperspectives.com Kool-Aid -Flavored I-Valex -2 Website: dietspec.com Yield: 16 fl oz Medical Food Taste Connections, LLC 40 g I-Valex-2 • Add chocolate or strawberry syrup. Phone: (310) 413-6499 3 Tbsp, level, sugar1 • Mix I-Valex with fruit to make a “smoothie.” Fax: (310) 318-8407 1/2 tsp Kool-Aid or Wyler’s Unsweetened Soft Drink Mix2 • Freeze flavored medical food into “slushies” or Email: [email protected] Add water (room temperature) to ingredients to make 16 fl “popsicles.” Website: tasteconnections.com oz. Mix in a blender at lowest speed no more than 4 seconds. • Add dry I-Valex to pudding (lemon, tapioca, Or, shake briskly in a closed container for 10 to 12 seconds. vanilla, etc) mixture. Prepare pudding with non- Serve chilled. dairy creamer. Nutrient 16 fl oz Use low-protein food lists to calculate LEU content Lysine, mg 0 of flavorings. Protein, g 12 Energy, kcal 308 1 Osmolality (concentration of particles in solution) may be too high if more sugar is added, which may cause bloating and diarrhea. 2 The amount of drink mix may be varied according to taste preference. Jell-O, Kool-Aid, Popsicles, Tang, Tylenol, Kuvan, NutraSweet, and Wyler’s are not registered trademarks of Abbott Laboratories. 17 16

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